Search on: KERATODERMA PALMOPLANTAR, PUNCTATE TYPE 2 
Descriptors Found: 1
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 1 / 1 DeCS     
Descriptor English:   Porokeratosis 
Descriptor Spanish:   Poroqueratosis 
Descriptor Portuguese:   Poroceratose 
Synonyms English:   Disseminated Superficial Actinic Porokeratosis
Keratoderma Palmoplantar, Punctate Type 2
Linear Porokeratosis
Mibelli Porokeratosis
Palmoplantar Porokeratosis
Porokeratosis Palmaris et Plantaris Disseminata
Porokeratosis Plantaris Palmaris et Disseminata
Porokeratosis Plantaris, Palmaris, Et Disseminata
Porokeratosis of Mibelli
Porokeratosis, Disseminated Superficial Actinic
Porokeratosis, Disseminated Superficial Actinic 2
Porokeratosis, Disseminated Superficial Actinic, 2
Porokeratosis, Linear
Porokeratosis, Mibelli
Porokeratosis, Palmar, Plantar, And Disseminated 1
Porokeratosis, Palmoplantar
Porokeratosis, Punctate
Punctate Porokeratosis
Type 2 Punctate PPK  
Tree Number:   C16.320.850.730
C17.800.428.750
C17.800.827.730
Definition English:   A heritable disorder of faulty keratinization characterized by the proliferation of abnormal clones of KERATINOCYTES and lesions showing varying atrophic patches surrounded by an elevated, keratotic border. These keratotic lesions can progress to overt cutaneous neoplasm. Several clinical variants are recognized, including porokeratosis of Mibelli, linear porokeratosis, disseminated superficial actinic porokeratosis, palmoplantar porokeratosis, and punctate porokeratosis. 
Indexing Annotation English:   do not confuse with PARAKERATOSIS
History Note English:   93 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications DI diagnosis
DG diagnostic imaging DH diet therapy
DT drug therapy EC economics
EM embryology EN enzymology
EP epidemiology EH ethnology
ET etiology GE genetics
HI history IM immunology
ME metabolism MI microbiology
MO mortality NU nursing
PS parasitology PA pathology
PP physiopathology PC prevention & control
PX psychology RT radiotherapy
RH rehabilitation SU surgery
TH therapy UR urine
VE veterinary VI virology
Record Number:   30610 
Unique Identifier:   D017499 

Occurrence in VHL:
 

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